| 产品详情 |
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| Product Name | Recombinant Human Lysosomal alpha-glucosidase (GAA) , partial |
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| Description | MW: 105,324 Da. Purity >85% (SDS-PAGE). This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe s disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. |
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| Size | 0.5 mg (E-Coli), 0.05 mg (Baculovirus), 0.5 mg (Yeast), 0.05 mg (Mammalian-Cell), 1 mg (E-Coli) |
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| Concentration | n/a |
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| Applications | n/a |
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| Other Names | [lysosomal alpha-glucosidase preproprotein; Lysosomal alpha-glucosidase; lysosomal alpha-glucosidase; glucosidase alpha, acid; Acid maltase; Aglucosidase alfa] |
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| Gene, Accession, CAS # | GAA, Gene ID: 2548, Accession: NP_000143.2 |
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| Catalog # | MBS948153 |
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| Order / More Info | Recombinant Human Lysosomal alpha-glucosidase (GAA) , partial from MYBIOSOURCE INC. |
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| Product Specific References | n/a |
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