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| Product Name | Recombinant Human alpha-Galactosidase A / GLA Protein (His tag) |
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| Description | MW: 35,011 Da. Purity >97 % as determined by SDS-PAGE. Background: Alpha-galactosidase A, also known as Alpha-D-galactoside galactohydrolase, Alpha-D-galactosidase A, Melibiase and GLA, is a member of the glycosyl hydrolase 27 family. GLA is used as a long-term enzyme replacement therapy in patients with a confirmed diagnosis of Fabry disease. Defects in GLA are the cause of Fabry disease (FD) which is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The dis |
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| Size | 0.02 mg, 0.05 mg |
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| Concentration | n/a |
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| Applications | The secreted recombinant human GLA consists of 409 amino acids and has a predicted molecular mass of 46.8 kDa. In SDS-PAGE under reducing conditions, it migrates as an approximately 50 kDa band. |
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| Other Names | [GALA] |
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| Gene, Accession, CAS # | GLA, Gene ID: 5618, Accession: NP_000940.1 |
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| Catalog # | MBS2545582 |
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| Order / More Info | Recombinant Human alpha-Galactosidase A / GLA Protein (His tag) from MYBIOSOURCE INC. |
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| Product Specific References | n/a |
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