| 产品详情 |
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| Product Name | Recombinant Mouse L-2-hydroxyglutarate dehydrogenase, mitochondrial (L2hgdh) |
| Description | 53-464aa, Full Length of Mature Protein. MW: 50,899 Da. Purity >85% (SDS-PAGE). This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation. |
| Size | 0.05 mg (E-Coli), 0.05 mg (Baculovirus), 0.2 mg (E-Coli), 0.5 mg (E-Coli), 0.2 mg (Yeast) |
| Concentration | n/a |
| Applications | n/a |
| Other Names | [L-2-hydroxyglutarate dehydrogenase, mitochondrial; L-2-hydroxyglutarate dehydrogenase, mitochondrial; L-2-hydroxyglutarate dehydrogenase, mitochondrial; L-2-hydroxyglutarate dehydrogenase; Duranin] |
| Gene, Accession, CAS # | L2hgdh, Gene ID: 217666, Accession: NP_663418.1 |
| Catalog # | MBS1341803 |
| Price | |
| Order / More Info | Recombinant Mouse L-2-hydroxyglutarate dehydrogenase, mitochondrial (L2hgdh) from MYBIOSOURCE INC. |
| Product Specific References | n/a |
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