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| Product Name | SCO2, Recombinant, Human, aa42-266, His-Tag (Protein SCO2 homolog, Mitochondrial, SCO1L) |
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| Description | Purity ~90% (SDS-PAGE). SCO2 protein belongs to the SCO1/2 family of proteins. Both SCO1 and SCO2 proteins are located on the inner membrane of the mitochondria and plays a crucial role in copper insertion or transport to the active site of cytochrome c oxidase (COX). Defects in SCO2 are the cause of fatal infantile cardioencephalomyopathy with cytochrome c oxidase deficiency (FIC). This disease is characterized by hypertrophic cardiomyopathy, lactic acidosis, and gliosis. Heart and skeletal muscle show reductions in cytochrome c oxidase (COX) activity, whereas liver and fibroblasts show mild COX deficiencies. Source: Recombinant protein corresponding to aa42-266 from human SCO2, fused to His-tag at N-terminal expressed in E. coli. Molecular Weight: ~27.4kD (246aa) AA |
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| Size | 50ug, 250ug |
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| Concentration | n/a |
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| Applications | n/a |
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| Other Names | n/a |
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| Gene, Accession, CAS # | Accession: NP_005129 |
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| Catalog # | 351491 |
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| Order / More Info | SCO2, Recombinant, Human, aa42-266, His-Tag (Protein SCO2 homolog, Mitochondrial, SCO1L) from UNITED STATES BIOLOGICAL |
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| Product Specific References | n/a |
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